Taiwan Journal of Ophthalmology

: 2020  |  Volume : 10  |  Issue : 3  |  Page : 181--183

Orbital hybrid peripheral nerve sheath tumors

Kai Ching Peter Leung, Tak Chuen Simon Ko 
 Department of Ophthalmology, Tung Wah Eastern Hosptial, Causewaybay, Hong Kong

Correspondence Address:
Dr. Kai Ching Peter Leung
Department Of Ophthalmology, Tung Wah Eastern Hospital, Causewaybay
Hong Kong

Hybrid peripheral nerve sheath tumors (HPNST) are recently classified tumors from the World Health Organization Classification of soft tissue tumors that display combined features of more than one peripheral nerve sheath tumor. Acknowledgment is important because of its association with the development of neurofibromatosis type 1, type 2, and schwannomatosis. Orbital involvement is rare and only six cases of HPNST have been documented on literature. This article serves to review the pathophysiology, clinical manifestation, diagnosis, treatment, and prognosis of this infrequent but important orbital tumor.

How to cite this article:
Leung KC, Ko TC. Orbital hybrid peripheral nerve sheath tumors.Taiwan J Ophthalmol 2020;10:181-183

How to cite this URL:
Leung KC, Ko TC. Orbital hybrid peripheral nerve sheath tumors. Taiwan J Ophthalmol [serial online] 2020 [cited 2020 Oct 28 ];10:181-183
Available from: https://www.e-tjo.org/article.asp?issn=2211-5056;year=2020;volume=10;issue=3;spage=181;epage=183;aulast=Leung;type=0